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RIPK3 Contributes to Lyso-Gb3-Induced Podocyte Death

Fabry disease is a lysosomal storage disease with an X-linked heritage caused by absent or decreased activity of lysosomal enzymes named alpha-galactosidase A (α-gal A). Among the various manifestations of Fabry disease, Fabry nephropathy significantly affects patients’ morbidity and mortality. The...

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Autori principali: So-Young Kim, Samel Park, Seong-Woo Lee, Ji-Hye Lee, Eun Soo Lee, Miri Kim, Youngjo Kim, Jeong Suk Kang, Choon Hee Chung, Jong-Seok Moon, Eun Young Lee
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI AG 2021-01-01
Serie:Cells
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Accesso online:https://www.mdpi.com/2073-4409/10/2/245
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