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Airway disease phenotypes in animal models of cystic fibrosis

Abstract In humans, cystic fibrosis (CF) lung disease is characterised by chronic infection, inflammation, airway remodelling, and mucus obstruction. A lack of pulmonary manifestations in CF mouse models has hindered investigations of airway disease pathogenesis, as well as the development and testi...

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Detalhes bibliográficos
Principais autores: Alexandra McCarron, Martin Donnelley, David Parsons
Formato: Artigo
Idioma:Inglês
Publicado em: BMC 2018-04-01
coleção:Respiratory Research
Assuntos:
Acesso em linha:http://link.springer.com/article/10.1186/s12931-018-0750-y
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