Codi QR

Use of Sirolimus and Immunoglobulin Replacement Therapy (IRT) in Patients with Activated Phosphoinositide 3-Kinase Delta Syndrome (APDS): A Systematic Literature Review (SLR)

IntroductionActivated Phosphoinositide 3-Kinase Delta Syndrome (APDS), a rare inborn error of immunity, is associated with immunodeficiency and immune dysregulation. Clinical management includes symptomatic treatment with immunoglobulin replacement therapy (IRT) and sirolimus, neither of which is ap...

Descripció completa

Guardat en:
Dades bibliogràfiques
Autors principals: Nicholas L. Hartog, Konrad Pisarczyk, Mike Samad, Katerina Vlachopoulou, Rachel Beckerman, Amanda Harrington
Format: Artigo
Idioma:Inglês
Publicat: Rockefeller University Press 2026-05-01
Col·lecció:Journal of Human Immunity
Accés en línia:https://rupress.org/jhi/article/2/CIS2026/eCIS2026abstract.112/281913/Use-of-Sirolimus-and-Immunoglobulin-Replacement
Etiquetes: Afegir etiqueta
Sense etiquetes, Sigues el primer a etiquetar aquest registre!