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Pacemaker Implantation in Juvenile Neuronal Ceroid Lipofuscinosis (CLN3)–A Long-Term Follow-Up Study

It is well documented that deteriorating heart function due to deposition of ceroid lipopigment is a significant co-morbidity in Juvenile Neuronal Ceroid Lipofuscinosis (CLN3 disease) although the exact disease mechanisms remain unknown in any NCL form. An increasing frequency of cardiac conduction...

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Autores principales: Mette Møller Handrup, Henning Mølgaard, Brian N. Andersen, John R. Ostergaard
Formato: Artigo
Lenguaje:Inglês
Publicado: Frontiers Media S.A. 2022-03-01
Colección:Frontiers in Neurology
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Acceso en línea:https://www.frontiersin.org/articles/10.3389/fneur.2022.846240/full
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