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Decreased N-TAF1 expression in X-linked dystonia-parkinsonism patient-specific neural stem cells

X-linked dystonia-parkinsonism (XDP) is a hereditary neurodegenerative disorder involving a progressive loss of striatal medium spiny neurons. The mechanisms underlying neurodegeneration are not known, in part because there have been few cellular models available for studying the disease. The XDP ha...

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Detalhes bibliográficos
Principais autores: Naoto Ito, William T. Hendriks, Jyotsna Dhakal, Christine A. Vaine, Christina Liu, David Shin, Kyle Shin, Noriko Wakabayashi-Ito, Marisela Dy, Trisha Multhaupt-Buell, Nutan Sharma, Xandra O. Breakefield, D. Cristopher Bragg
Formato: Artigo
Idioma:Inglês
Publicado em: The Company of Biologists 2016-04-01
coleção:Disease Models & Mechanisms
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Acesso em linha:http://dmm.biologists.org/content/9/4/451
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