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Murine models of sickle cell disease and beta‐thalassemia demonstrate pulmonary hypertension with distinctive features

Sickle cell anemia and β‐thalassemia intermedia are very different genetically determined hemoglobinopathies predisposing to pulmonary hypertension. The etiologies responsible for the associated development of pulmonary hypertension in both diseases are multi‐factorial with extensive mechanistic con...

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Autors principals: Paul W. Buehler, Delaney Swindle, David I. Pak, Mehdi A. Fini, Kathryn Hassell, Rachelle Nuss, Rebecca B. Wilkerson, Angelo D’Alessandro, David C. Irwin
Format: Artigo
Idioma:Inglês
Publicat: Wiley 2021-10-01
Col·lecció:Pulmonary Circulation
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Accés en línia:https://doi.org/10.1177/20458940211055996
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