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Primary intestinal lymphangiectasia: French National Diagnosis and Care Protocol (PNDS; Protocole National de Diagnostic et de Soins)

Abstract Background Primary intestinal lymphangiectasia or Waldmann’s disease (ORPHA code: 90362) is a very rare disorder of unknown etiology, characterized by digestive lymphatic vessel dilations. Main body of the abstract The objective of the French National Diagnosis and Care Protocol (PNDS; Prot...

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Principais autores: Stéphane Vignes, Mathieu Uzzan, Lionel Arrivé, Françoise Le Pimpec-Barthes, Claire Fieschi, Guillaume Lefèvre, Manon Javalet, Joanna Bettolo, Béatrice Dubern
Formato: Artigo
Idioma:Inglês
Publicado: BMC 2025-07-01
Series:Orphanet Journal of Rare Diseases
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Acceso en liña:https://doi.org/10.1186/s13023-025-03657-9
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