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In vivo cerebellar circuit function is disrupted in an mdx mouse model of Duchenne muscular dystrophy

Duchenne muscular dystrophy (DMD) is a debilitating and ultimately lethal disease involving progressive muscle degeneration and neurological dysfunction. DMD is caused by mutations in the dystrophin gene, which result in extremely low or total loss of dystrophin protein expression. In the brain, dys...

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Autori principali: Trace L. Stay, Lauren N. Miterko, Marife Arancillo, Tao Lin, Roy V. Sillitoe
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Company of Biologists 2020-02-01
Serie:Disease Models & Mechanisms
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Accesso online:http://dmm.biologists.org/content/13/2/dmm040840
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