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Progranulin acts as a shared chaperone and regulates multiple lysosomal enzymes

Multifunctional factor progranulin (PGRN) plays an important role in lysosomes, and its mutations and insufficiency are associated with lysosomal storage diseases, including neuronal ceroid lipofuscinosis and Gaucher disease (GD). The first breakthrough in understanding the molecular mechanisms of P...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Jinlong Jian, Aubryanna Hettinghouse, Chuan-ju Liu
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: KeAi Communications Co., Ltd. 2017-09-01
Saila:Genes and Diseases
Gaiak:
Sarrera elektronikoa:http://www.sciencedirect.com/science/article/pii/S2352304217300363
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