Efficacy of elexacaftor/tezacaftor/ivacaftor in non-cystic fibrosis bronchiectasis patients with a single pathogenic CFTR mutation: a retrospective cohort analysis

Introduction It has previously been established that there is an increased incidence of mutations in the cystic fibrosis transmembrane regulator (CFTR) gene amongst patients with non-cystic fibrosis bronchiectasis (NCFB). With the advent of new highly effective CFTR modulators, specifically elexacaf...

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Номзүйн дэлгэрэнгүй

Үндсэн зохиолчид:	Lena Papadakis, Isabel Neuringer, Hang Lee, Anne O'Donnell, Julia Zweifach, Brenden Lawton, Leonard Sicilian, Rocio Hurtado, Tayler Stander, Lindsay Bringhurst, Christopher Richards
Формат:	Artigo
Хэл сонгох:	Inglês
Хэвлэсэн:	European Respiratory Society 2025-11-01
Цуврал:	ERJ Open Research
Онлайн хандалт:	https://doi.org/10.1183/23120541.00007-2025
Шошгууд:	Шошго нэмэх Шошго байхгүй, Энэхүү баримтыг шошголох эхний хүн болох!