Efficacy of elexacaftor/tezacaftor/ivacaftor in non-cystic fibrosis bronchiectasis patients with a single pathogenic CFTR mutation: a retrospective cohort analysis

Introduction It has previously been established that there is an increased incidence of mutations in the cystic fibrosis transmembrane regulator (CFTR) gene amongst patients with non-cystic fibrosis bronchiectasis (NCFB). With the advent of new highly effective CFTR modulators, specifically elexacaf...

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Autores principales:	Lena Papadakis, Isabel Neuringer, Hang Lee, Anne O'Donnell, Julia Zweifach, Brenden Lawton, Leonard Sicilian, Rocio Hurtado, Tayler Stander, Lindsay Bringhurst, Christopher Richards
Formato:	Artigo
Lenguaje:	Inglês
Publicado:	European Respiratory Society 2025-11-01
Colección:	ERJ Open Research
Acceso en línea:	https://doi.org/10.1183/23120541.00007-2025
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