Impaired intestinal free fatty acid transport followed by chylomicron malformation, not pancreatic insufficiency, cause metabolic defects in cystic fibrosis

Intestinal disease is one of the earliest manifestations of cystic fibrosis (CF) in children and is closely tied to deficits in growth and nutrition, both of which are directly linked to future mortality. Patients are treated aggressively with pancreatic enzyme replacement therapy and a high-fat die...

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Ngā kaituhi matua:	Lihong Teng, Nikolaos Dedousis, Aneseh Adeshirlarijaney, Jitendra S. Kanshana, Min Liu, Craig A. Hodges, Alison B. Kohan
Hōputu:	Artigo
Reo:	Inglês
I whakaputaina:	Elsevier 2024-07-01
Rangatū:	Journal of Lipid Research
Ngā marau:	fatty acid transport cystic fibrosis intestine chylomicrons lipid metabolism dietary fat
Urunga tuihono:	http://www.sciencedirect.com/science/article/pii/S0022227524000567
Ngā Tūtohu:	Tāpirihia he Tūtohu Kāore He Tūtohu, Me noho koe te mea tuatahi ki te tūtohu i tēnei pūkete!