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Interventional pulmonary procedures and their outcomes in patients with STAT3 hyper IgE syndrome

Abstract Background STAT3 hyperimmunoglobulin E syndrome (STAT3-HIES) also referred to as autosomal dominant HIES (AD-HIES) is an inborn error of immunity characterized by the classic triad of eczema, frequent opportunistic infections, and elevated serum IgE levels. As a consequence of lung sequels...

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Bibliografiset tiedot
Päätekijät: Seyed Alireza Mahdaviani, Soodeh Ghadimi, Mazdak Fallahi, Seyedeh Atefeh Hashemi-Moghaddam, Zahra Chavoshzadeh, Anne Puel, Nima Rezaei, Mahsa Rekabi, Zahra Daneshmandi, Kambiz Sheikhy, Abolghasem Daneshvar Kakhki, Seyed Reza Saghebi, Saviz Pejhan, Mahnaz Jamee
Aineistotyyppi: Artigo
Kieli:Inglês
Julkaistu: BMC 2023-09-01
Sarja:BMC Surgery
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Linkit:https://doi.org/10.1186/s12893-023-02193-2
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