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Systematic review of the incidence and clinical risk predictors of atrial fibrillation and permanent pacemaker implantation for bradycardia in Fabry disease

Introduction Fabry disease (FD) is an X-linked lysosomal storage disorder caused by enzyme deficiency, leading to glycosphingolipid accumulation. Cardiac accumulation triggers local tissue injury, electrical instability and arrhythmia. Bradyarrhythmia and atrial fibrillation (AF) incidence are repor...

Whakaahuatanga katoa

I tiakina i:
Ngā taipitopito rārangi puna kōrero
Ngā kaituhi matua: Ravi Vijapurapu, Derralynn A Hughes, Tarekegn Geberhiwot, Richard Paul Steeds, Dipak Kotecha, Adrian Warfield, James Moon, Peter Woolfson, Polyvios Demetriades, Ashwin Roy, Joseph de Bono
Hōputu: Artigo
Reo:Inglês
I whakaputaina: BMJ Publishing Group 2023-11-01
Rangatū:Open Heart
Urunga tuihono:https://openheart.bmj.com/content/10/2/e002316.full
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