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Systematic review of the incidence and clinical risk predictors of atrial fibrillation and permanent pacemaker implantation for bradycardia in Fabry disease

Introduction Fabry disease (FD) is an X-linked lysosomal storage disorder caused by enzyme deficiency, leading to glycosphingolipid accumulation. Cardiac accumulation triggers local tissue injury, electrical instability and arrhythmia. Bradyarrhythmia and atrial fibrillation (AF) incidence are repor...

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Detaylı Bibliyografya
Asıl Yazarlar: Ravi Vijapurapu, Derralynn A Hughes, Tarekegn Geberhiwot, Richard Paul Steeds, Dipak Kotecha, Adrian Warfield, James Moon, Peter Woolfson, Polyvios Demetriades, Ashwin Roy, Joseph de Bono
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: BMJ Publishing Group 2023-11-01
Seri Bilgileri:Open Heart
Online Erişim:https://openheart.bmj.com/content/10/2/e002316.full
Etiketler: Etiketle
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