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Dietary and Therapeutic Management of Glycogen Storage Disease Type IX: Analysis of a Systematic Review

Background/Objectives: Glycogen storage disease type IX (GSD IX) is an inherited metabolic disorder characterized by marked clinical heterogeneity and variable severity. Dietary therapy is considered the cornerstone of management, but evidence on treatment strategies, efficacy, and safety remains li...

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Hauptverfasser: Giulia Montanari, Andrea Zanaroli, Egidio Candela, Giacomo Biasucci, Federico Baronio, Rita Ortolano, Marcello Lanari
Format: Artigo
Sprache:Inglês
Veröffentlicht: MDPI AG 2026-05-01
Schriftenreihe:Children
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Online-Zugang:https://www.mdpi.com/2227-9067/13/5/648
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