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Mitochondrial Dysfunctions in Human Primary Coenzyme Q<sub>10</sub> Deficiencies

Coenzyme Q<sub>10</sub> (CoQ<sub>10</sub>) is an essential lipid-soluble molecule that plays a central role in mitochondrial energy production as a mobile electron carrier. In addition to its bioenergetic function, CoQ<sub>10</sub> participates in antioxidant defense, redox homeostasis, lipid and nu...

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Autori principali: Fanny Fontaine, Romain Pénicaud, Stéphane Allouche
Natura: Artigo
Lingua:Inglês
Pubblicazione: MDPI AG 2026-02-01
Serie:Biomolecules
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Accesso online:https://www.mdpi.com/2218-273X/16/2/302
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