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Mitochondrial Dysfunctions in Human Primary Coenzyme Q<sub>10</sub> Deficiencies

Coenzyme Q<sub>10</sub> (CoQ<sub>10</sub>) is an essential lipid-soluble molecule that plays a central role in mitochondrial energy production as a mobile electron carrier. In addition to its bioenergetic function, CoQ<sub>10</sub> participates in antioxidant defense, redox homeostasis, lipid and nu...

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Bibliografski detalji
Glavni autori: Fanny Fontaine, Romain Pénicaud, Stéphane Allouche
Format: Artigo
Jezik:Inglês
Izdano: MDPI AG 2026-02-01
Serija:Biomolecules
Teme:
Online pristup:https://www.mdpi.com/2218-273X/16/2/302
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