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Langerhans cell histiocytosis confined to extrahepatic bile duct causing sclerosing cholangitis in child: a case report

Abstract Background Langerhans cell histiocytosis (LCH) is an abnormal accumulation of Langerhans cells in various organs that sometimes induces organ dysfunction. LCH can affect the liver, resulting in sclerosing cholangitis and biliary cirrhosis. However, liver and bile duct involvement is usually...

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Hlavní autoři: Masakazu Murakami, Shun Onishi, Yuki Ohya, Seiichi Kawabata, Kaori Isono, Yasuhiko Sugawara, Tsuguharu Asato, Yumi Honda, Yoshiki Mikami, Yukihiro Inomata, Taizo Hibi, Satoshi Ieiri
Médium: Artigo
Jazyk:Inglês
Vydáno: Japan Surgical Society 2020-06-01
Edice:Surgical Case Reports
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On-line přístup:http://link.springer.com/article/10.1186/s40792-020-00899-6
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