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Transthyretin Amyloidosis: Update on the Clinical Spectrum, Pathogenesis, and Disease-Modifying Therapies

Abstract ATTR amyloidosis is caused by systemic deposition of transthyretin (TTR) and comprises ATTRwt (wt for wild-type) amyloidosis, ATTRv (v for variant) amyloidosis, and acquired ATTR amyloidosis after domino liver transplantation. ATTRwt amyloidosis has classically been regarded as cardiomyopat...

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Detalles Bibliográficos
Principais autores: Haruki Koike, Masahisa Katsuno
Formato: Artigo
Idioma:Inglês
Publicado: Adis, Springer Healthcare 2020-09-01
Series:Neurology and Therapy
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Acceso en liña:https://doi.org/10.1007/s40120-020-00210-7
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