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Autoimmune lymphoproliferative immunodeficiencies (ALPID) in childhood: breakdown of immune homeostasis and immune dysregulation

Abstract Many inborn errors of immunity (IEI) manifest with hallmarks of both immunodeficiency and immune dysregulation due to uncontrolled immune responses and impaired immune homeostasis. A subgroup of these disorders frequently presents with autoimmunity and lymphoproliferation (ALPID phenotype)....

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Autori principali: Vasil Toskov, Stephan Ehl
Natura: Artigo
Lingua:Inglês
Pubblicazione: SpringerOpen 2023-09-01
Serie:Molecular and Cellular Pediatrics
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Accesso online:https://doi.org/10.1186/s40348-023-00167-1
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