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Myriocin Effect on Tvrm4 Retina, an Autosomal Dominant Pattern of Retinitis Pigmentosa

Tvrm4 mice, a model of autosomal dominant retinitis pigmentosa (RP), carry a mutation of Rhodopsin gene that can be activated by brief exposure to very intense light. Here, we test the possibility of an anatomical, metabolic, and functional recovery by delivering to degenerating Tvrm4 animals, Myrio...

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主要な著者: Ilaria Piano, Vanessa D’Antongiovanni, Elena Novelli, Martina Biagioni, Michele Dei Cas, Rita Clara Paroni, Riccardo Ghidoni, Enrica Strettoi, Claudia Gargini
フォーマット: Artigo
言語:Inglês
出版事項: Frontiers Media S.A. 2020-05-01
シリーズ:Frontiers in Neuroscience
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オンライン・アクセス:https://www.frontiersin.org/article/10.3389/fnins.2020.00372/full
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