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TAFRO Syndrome Without Pathology Supporting Castleman Disease: To Be Treated as Idiopathic Multicentric Castleman Disease-TAFRO or a Distinct Disease Entity?

Objective: TAFRO syndrome, entailing thrombocytopenia, anasarca, fever, reticulin fibrosis, and organomegaly, was previously considered a subtype of idiopathic multicentric Castleman disease (iMCD-TAFRO), with the diagnosis requiring pathology supporting Castleman disease. However, lymph node biopsi...

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Autori principali: Siyuan Li, Yuhan Gao, Yue Dang, Lu Zhang, Jian Li
Natura: Artigo
Lingua:Inglês
Pubblicazione: Turkish Society of Hematology 2025-03-01
Serie:Turkish Journal of Hematology
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Accesso online:https://www.tjh.com.tr/jvi.aspx?un=TJH-07504&volume=42&issue=1
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