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Concurrent idiopathic multicentric Castleman disease with TAFRO and Sjögren’s syndrome in a young patient: a challenging diagnostic overlap

Background: Idiopathic multicentric Castleman disease (iMCD) with TAFRO syndrome (characterized by thrombocytopenia, anasarca, fever, reticulin fibrosis/renal failure, organomegaly) is a recently described disorder. The diagnostic criteria for iMCD-TAFRO exclude patients with concomitant autoimmune...

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Autors principals: Maria Carolina Carvalho, Matilde Coimbra, João Fernandes Serodio, José Delgado Alves
Format: Artigo
Idioma:Inglês
Publicat: SMC MEDIA SRL 2026-02-01
Col·lecció:European Journal of Case Reports in Internal Medicine
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Accés en línia:https://www.ejcrim.com/index.php/EJCRIM/article/view/6166
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