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Pulmonary vascular dysfunction without pulmonary hypertension: A distinct phenotype in idiopathic pulmonary fibrosis

Abstract Pulmonary vascular dysfunction in the absence of pulmonary hypertension (PH) has been observed in patients with idiopathic pulmonary fibrosis (IPF). We describe the prevalence and etiology of elevated pulmonary vascular resistance (PVR) without PH among patients with IPF. Hemodynamic, echoc...

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Главные авторы: Steven D. Nathan, Benham Tehrani, Qiong Zhao, Rafael Arias, Dennis Kim, Antonia Pellegrini, Ashley Claire Collins, Jack Diviney, Shourjo Chakravorty, Vikramjit Khangoora, Oksana A. Shlobin, Christopher Thomas, Ben R. Lavon, Christopher S. King, Abhimanyu Chandel
Формат: Artigo
Язык:Inglês
Опубликовано: Wiley 2024-01-01
Серии:Pulmonary Circulation
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Online-ссылка:https://doi.org/10.1002/pul2.12311
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