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Combining angiotensin receptor blockade and enzyme replacement therapy for vascular disease in mucopolysaccharidosis type I

Vascular involvement in the genetic disorder mucopolysaccharidosis type I (MPS I) has features of atherosclerotic disease near branch points of arterial vasculature, such as intimal thickening with disruption of the internal elastic lamina, and proliferation of macrophages and myofibroblasts. Inflam...

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Detaylı Bibliyografya
Asıl Yazarlar: Sarah C. Hurt, Moin U. Vera, Steven Q. Le, Shih-hsin Kan, Quang Bui, Patricia I. Dickson
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: Elsevier 2024-03-01
Seri Bilgileri:Molecular Genetics and Metabolism Reports
Konular:
Online Erişim:http://www.sciencedirect.com/science/article/pii/S2214426923000824
Etiketler: Etiketle
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