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Combining angiotensin receptor blockade and enzyme replacement therapy for vascular disease in mucopolysaccharidosis type I

Vascular involvement in the genetic disorder mucopolysaccharidosis type I (MPS I) has features of atherosclerotic disease near branch points of arterial vasculature, such as intimal thickening with disruption of the internal elastic lamina, and proliferation of macrophages and myofibroblasts. Inflam...

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Principais autores: Sarah C. Hurt, Moin U. Vera, Steven Q. Le, Shih-hsin Kan, Quang Bui, Patricia I. Dickson
Format: Artigo
Jezik:Inglês
Izdano: Elsevier 2024-03-01
Serija:Molecular Genetics and Metabolism Reports
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Online dostop:http://www.sciencedirect.com/science/article/pii/S2214426923000824
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