Spectrum of Respiratory Involvement in Ehlers–Danlos Syndrome: Insights From a Case Report

Vascular Ehlers–Danlos syndrome (vEDS) is a rare connective tissue disorder characterized by type III collagen deficiency and marked vascular fragility, which can lead to atypical thoracic manifestations and diagnostic uncertainty. We report a 30-year-old man who initially presented with an ischemic...

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Detalhes bibliográficos

Principais autores:	Arianna Andrade, Isabel Pava-Bernat, Luis del Carpio, Galo Granados, Antía Ferreiro-Posse
Formato:	Artigo
Idioma:	Inglês
Publicado em:	Elsevier 2026-04-01
coleção:	Open Respiratory Archives
Assuntos:	Síndrome de Ehlers-Danlos vascular Hematoma intrapulmonar Nódulos pulmonares
Acesso em linha:	http://www.sciencedirect.com/science/article/pii/S265966362600069X
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