Spectrum of Respiratory Involvement in Ehlers–Danlos Syndrome: Insights From a Case Report
Vascular Ehlers–Danlos syndrome (vEDS) is a rare connective tissue disorder characterized by type III collagen deficiency and marked vascular fragility, which can lead to atypical thoracic manifestations and diagnostic uncertainty. We report a 30-year-old man who initially presented with an ischemic...
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| Autors principals: | , , , , |
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| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
Elsevier
2026-04-01
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| Col·lecció: | Open Respiratory Archives |
| Matèries: | |
| Accés en línia: | http://www.sciencedirect.com/science/article/pii/S265966362600069X |
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