Early glial activation, synaptic changes and axonal pathology in the thalamocortical system of Niemann–Pick type C1 mice

Por Pressey, Sarah N.R., Smith, David A., Wong, Andrew M.S., Platt, Frances M., Cooper, Jonathan D.
Publicado em 2012

Correction: Disruption of the Autophagy-Lysosome Pathway Is Involved in Neuropathology of the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis

Por Thelen, Melanie, Damme, Markus, Schweizer, Michaela, Hagel, Christian, Wong, Andrew M.S., Cooper, Jonathan D., Braulke, Thomas, Galliciotti, Giovanna
Publicado em 2012

Disruption of the Autophagy-Lysosome Pathway Is Involved in Neuropathology of the nclf Mouse Model of Neuronal Ceroid Lipofuscinosis

Por Thelen, Melanie, Daμμe, Markus, Schweizer, Michaela, Hagel, Christian, Wong, Andrew M.S., Cooper, Jonathan D., Braulke, Thomas, Galliciotti, Giovanna
Publicado em 2012

Immunosuppression alters disease severity in juvenile Batten disease mice

Por Seehafer, Sabrina S., Ramirez-Montealegre, Denia, Wong, Andrew MS, Chan, Chun-Hung, Castaneda, Julian, Horak, Michael, Ahmadi, Sarah M, Lim, Ming J, Cooper, Jonathan D, Pearce, David A
Publicado em 2011

An Anti-Neuroinflammatory That Targets Dysregulated Glia Enhances the Efficacy of CNS-Directed Gene Therapy in Murine Infantile Neuronal Ceroid Lipofuscinosis

Por Macauley, Shannon L., Wong, Andrew M.S., Shyng, Charles, Augner, David P., Dearborn, Joshua T., Pearse, Yewande, Roberts, Marie S., Fowler, Stephen C., Cooper, Jonathan D., Watterson, D. Martin, Sands, Mark S.
Publicado em 2014

Partial Correction of the CNS Lysosomal Storage Defect in a Mouse Model of Juvenile Neuronal Ceroid Lipofuscinosis by Neonatal CNS Administration of an Adeno-Associated Virus Serot...

Por Sondhi, Dolan, Scott, Emma C., Chen, Alvin, Hackett, Neil R., Wong, Andrew M.S., Kubiak, Agnieszka, Nelvagal, Hemanth R., Pearse, Yewande, Cotman, Susan L., Cooper, Jonathan D., Crystal, Ronald G.
Publicado em 2014

Intravenous high-dose enzyme replacement therapy with recombinant palmitoyl-protein thioesterase reduces visceral lysosomal storage and modestly prolongs survival in a preclinical...

Por Hu, Jie, Lu, Jui-Yun, Wong, Andrew M.S., Hynan, Linda S., Birnbaum, Shari G., Yilmaz, Denis S., Streit, Barbara M., Lenartowicz, Ewelina M., Thompson, Thomas C.M., Cooper, Jonathan D., Hofmann, Sandra L.
Publicado em 2012

A novel, long-lived, and highly engraftable immunodeficient mouse model of mucopolysaccharidosis type I

Por Mendez, Daniel C, Stover, Alexander E, Rangel, Anthony D, Brick, David J, Nethercott, Hubert E, Torres, Marissa A, Khalid, Omar, Wong, Andrew MS, Cooper, Jonathan D, Jester, James V, Monuki, Edwin S, McGuire, Cian, Le, Steven Q, Kan, Shih-hsin, Dickson, Patricia I, Schwartz, Philip H
Publicado no Mol Ther Methods Clin Dev (2015)