Pharmacological Rescue of Conditionally Reprogrammed Cystic Fibrosis Bronchial Epithelial Cells

Por Gentzsch, Martina, Boyles, Susan E., Cheluvaraju, Chaitra, Chaudhry, Imron G., Quinney, Nancy L., Cho, Crescentia, Dang, Hong, Liu, Xuefeng, Schlegel, Richard, Randell, Scott H.
Publicado no Am J Respir Cell Mol Biol (2017)

Potentiator Ivacaftor Abrogates Pharmacological Correction of ΔF508 CFTR in Cystic Fibrosis

Por Cholon, Deborah M., Quinney, Nancy L., Fulcher, M. Leslie, Esther, Charles R., Das, Jhuma, Dokholyan, Nikolay V., Randell, Scott H., Boucher, Richard C., Gentzsch, Martina
Publicado no Sci Transl Med (2014)

Restoration of R117H CFTR folding and function in human airway cells through combination treatment with VX-809 and VX-770

Por Gentzsch, Martina, Ren, Hong Y., Houck, Scott A., Quinney, Nancy L., Cholon, Deborah M., Sopha, Pattarawut, Chaudhry, Imron G., Das, Jhuma, Dokholyan, Nikolay V., Randell, Scott H., Cyr, Douglas M.
Publicado no Am J Physiol Lung Cell Mol Physiol (2016)