Hermansky-Pudlak Syndrome Interstitial Pneumonia: It’s the Epithelium, Stupid!

Por Mahavadi, Poornima, Guenther, Andreas, Gochuico, Bernadette R.
Publicado em 2012

ADP-ribosylation of human defensin HNP-1 results in the replacement of the modified arginine with the noncoded amino acid ornithine

Por Stevens, Linda A., Levine, Rodney L., Gochuico, Bernadette R., Moss, Joel
Publicado em 2009

Prevalence of Uterine Leiomyomas in Lymphangioleiomyomatosis

Por Taveira-Dasilva, Angelo M., Rabel, Antoinette, Gochuico, Bernadette R., Avila, Nilo A., Moss, Joel
Publicado em 2011

Circulating Markers of Interstitial Lung Disease and Subsequent Risk of Lung Cancer

Por Shiels, Meredith S., Chaturvedi, Anil K., Katki, Hormuzd A., Gochuico, Bernadette R., Caporaso, Neil E., Engels, Eric A.
Publicado em 2011

Automated Quantification of High-Resolution CT Scan Findings in Individuals at Risk for Pulmonary Fibrosis

Por Rosas, Ivan O., Yao, Jianhua, Avila, Nilo A., Chow, Catherine K., Gahl, William A., Gochuico, Bernadette R.
Publicado em 2011

Impairment of Alveolar Macrophage Transcription in Idiopathic Pulmonary Fibrosis

Por Ren, Ping, Rosas, Ivan O., MacDonald, Sandra D., Wu, Hai-Ping, Billings, Eric M., Gochuico, Bernadette R.
Publicado em 2007

Oxidative Stress Alters Syndecan-1 Distribution in Lungs with Pulmonary Fibrosis

Por Kliment, Corrine R., Englert, Judson M., Gochuico, Bernadette R., Yu, Guoying, Kaminski, Naftali, Rosas, Ivan, Oury, Tim D.
Publicado em 2009

In vitro functional correction of Hermansky-Pudlak Syndrome type-1 by lentiviral-mediated gene transfer

Por Ikawa, Yasuhiro, Hess, Richard, Dorward, Heidi, Cullinane, Andrew R., Huizing, Marjan, Gochuico, Bernadette R., Gahl, William A., Candotti, Fabio
Publicado no Mol Genet Metab (2014)

Bleomycin and IL-1β–mediated pulmonary fibrosis is IL-17A dependent

Por Wilson, Mark S., Madala, Satish K., Ramalingam, Thirumalai R., Gochuico, Bernadette R., Rosas, Ivan O., Cheever, Allen W., Wynn, Thomas A.
Publicado em 2010

Glucose Transporter-1 Distribution in Fibrotic Lung Disease: Association With [(18)F]-2-Fluoro-2-Deoxyglucose-PET Scan Uptake, Inflammation, and Neovascularization

Por El-Chemaly, Souheil, Malide, Daniela, Yao, Jianhua, Nathan, Steven D., Rosas, Ivan O., Gahl, William A., Moss, Joel, Gochuico, Bernadette R.
Publicado em 2013

Transforming Growth Factor-β1 Downregulates Vascular Endothelial Growth Factor-D Expression in Human Lung Fibroblasts via the Jun NH(2)-Terminal Kinase Signaling Pathway

Por Cui, Ye, Osorio, Juan C, Risquez, Cristobal, Wang, Hao, Shi, Ying, Gochuico, Bernadette R, Morse, Danielle, Rosas, Ivan O, El-Chemaly, Souheil
Publicado em 2014

Extensive citrullination promotes immunogenicity of HSP90 through protein unfolding and exposure of cryptic epitopes()

Por Travers, Timothy S., Harlow, Lisa, Rosas, Ivan O., Gochuico, Bernadette R., Mikuls, Ted R., Bhattacharya, Sanjoy K., Camacho, Carlos J., Ascherman, Dana P.
Publicado no J Immunol (2016)

Epithelial Stress and Apoptosis Underlie Hermansky-Pudlak Syndrome–associated Interstitial Pneumonia

Por Mahavadi, Poornima, Korfei, Martina, Henneke, Ingrid, Liebisch, Gerhard, Schmitz, Gerd, Gochuico, Bernadette R., Markart, Philipp, Bellusci, Saverio, Seeger, Werner, Ruppert, Clemens, Guenther, Andreas
Publicado em 2010

Interstitial Lung Disease and Pulmonary Fibrosis in Hermansky-Pudlak Syndrome Type 2, an Adaptor Protein-3 Complex Disease

Por Gochuico, Bernadette R, Huizing, Marjan, Golas, Gretchen A, Scher, Charles D, Tsokos, Maria, Denver, Stacey D, Frei-Jones, Melissa J, Gahl, William A
Publicado em 2011

Pirfenidone for the treatment of Hermansky-Pudlak Syndrome pulmonary fibrosis

Por O’Brien, Kevin, Troendle, James, Gochuico, Bernadette R., Markello, Thomas C., Salas, Jose, Cardona, Hilda, Yao, Jianhua, Bernardini, Isa, Hess, Richard, Gahl, William A.
Publicado em 2011

Alveolar Macrophage Dysregulation in Hermansky-Pudlak Syndrome Type 1

Por Rouhani, Farshid N., Brantly, Mark L., Markello, Thomas C., Helip-Wooley, Amanda, O'Brien, Kevin, Hess, Richard, Huizing, Marjan, Gahl, William A., Gochuico, Bernadette R.
Publicado em 2009

Nuclear Localization of Vascular Endothelial Growth Factor-D and Regulation of c-Myc–Dependent Transcripts in Human Lung Fibroblasts

Por El-Chemaly, Souheil, Pacheco-Rodriguez, Gustavo, Malide, Daniela, Meza-Carmen, Victor, Kato, Jiro, Cui, Ye, Padilla, Philip I., Samidurai, Arun, Gochuico, Bernadette R., Moss, Joel
Publicado em 2014

Anti-citrullinated heat shock protein 90 antibodies identified in bronchoalveolar lavage fluid are a marker of lung-specific immune responses

Por Harlow, Lisa, Gochuico, Bernadette R., Rosas, Ivan O., Doyle, Tracy J., Osorio, Juan C., Travers, Timothy S., Camacho, Carlos C., Oddis, Chester V., Ascherman, Dana P.
Publicado no Clin Immunol (2014)

MAP1LC3B overexpression protects against Hermansky-Pudlak syndrome type-1-induced defective autophagy in vitro

Por Ahuja, Saket, Knudsen, Lars, Chillappagari, Shashi, Henneke, Ingrid, Ruppert, Clemens, Korfei, Martina, Gochuico, Bernadette R., Bellusci, Saverio, Seeger, Werner, Ochs, Matthias, Guenther, Andreas, Mahavadi, Poornima
Publicado no Am J Physiol Lung Cell Mol Physiol (2015)

Circulating Fibrocytes as Biomarker of Prognosis in Hermansky-Pudlak Syndrome

Por Trimble, Aaron, Gochuico, Bernadette R., Markello, Thomas C., Fischer, Roxanne, Gahl, William A., Lee, Jae K., Kim, Youngchul, Burdick, Marie D., Strieter, Robert M., Mehrad, Borna
Publicado no Am J Respir Crit Care Med (2014)