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Dyskeratosis congenita

Dyskeratosis congenita (DC) is a genetic syndrome with progressive multisystem involvement classically characterized by the clinical triad of oral leukoplakia, nail dystrophy, and reticular hyperpigmentation. Frequent complications are bone marrow failure, increased rate of malignancy, lung and live...

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Detalhes bibliográficos
Publicado no:Autopsy and Case Reports
Main Authors: Lorenzo Gitto, Robert Stoppacher, Timothy Eric Richardson, Serenella Serinelli
Formato: Artigo
Idioma:Inglês
Publicado em: Hospital Universitário da Universidade de São Paulo 2020
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Acesso em linha:https://www.redalyc.org/articulo.oa?id=576065838018
https://www.redalyc.org/journal/5760/576065838018/
https://www.redalyc.org/journal/5760/576065838018/html/
https://www.redalyc.org/journal/5760/576065838018/576065838018.epub
https://www.redalyc.org/journal/5760/576065838018/movil
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