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Anesthetic Management of a Patient with Harlequin Ichthyosis
Harlequin ichthyosis is a severe and often fatal form of congenital ichthyosis caused by defective lipid transport which results in a dysfunctional skin barrier. Patients who survive the neonatal period are predisposed to skin infections, sepsis, impaired thermoregulation, and dehydration. The uniqu...
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| Publicado en: | Case Rep Anesthesiol |
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| Autores principales: | , , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
Hindawi
2021
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC8328734/ https://ncbi.nlm.nih.gov/pubmed/34350038 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2021/9953320 |
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