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Quantitative Myocardial Perfusion in Fabry Disease

BACKGROUND: Fabry disease (FD) is an X-linked lysosomal storage disease resulting in tissue accumulation of sphingolipids. Key myocardial processes that lead to adverse outcomes in FD include storage, hypertrophy, inflammation, and fibrosis. These are quantifiable by multiparametric cardiovascular m...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Argitaratua izan da:Circ Cardiovasc Imaging
Egile Nagusiak: Knott, Kristopher D., Augusto, Joao B., Nordin, Sabrina, Kozor, Rebecca, Camaioni, Claudia, Xue, Hui, Hughes, Rebecca K., Manisty, Charlotte, Brown, Louise A.E., Kellman, Peter, Ramaswami, Uma, Hughes, Derralyn, Plein, Sven, Moon, James C.
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2019
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC8323709/
https://ncbi.nlm.nih.gov/pubmed/31269811
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCIMAGING.119.008872
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