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Comprehensive Risk Management in Arrhythmogenic Cardiomyopathy Associated With Autosomal Dominant Carvajal Syndrome: Protecting Families

In a 37-year-old cardiac arrest survivor with autosomal dominant Carvajal syndrome and arrhythmogenic cardiomyopathy, a desmoplakin mutation was identified. Cascade screening identified 2 affected family members and 2 healthy children carrying the mutation. Strategies for primary and secondary risk...

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Bibliografiske detaljer
Udgivet i:JACC Case Rep
Main Authors: De Gregorio, Maria Grazia, Girolami, Francesca, Tomberli, Benedetta, Rossi, Guendalina, Tomberli, Alessia, Baldini, Katia, Olivotto, Iacopo
Format: Artigo
Sprog:Inglês
Udgivet: Elsevier 2020
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC8302052/
https://ncbi.nlm.nih.gov/pubmed/34317383
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jaccas.2020.03.033
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