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A case of hereditary angioedema due to C1-inhibitor deficiency with recurrent abdominal pain diagnosed 40 years after the occurrence of the initial symptom

Hereditary angioedema due to C1-inhibitor deficiency (HAE-C1-INH) is a rare disease, which induces an acute attack of angioedema mediated by bradykinin. HAE-C1-INH can cause serious abdominal pain when severe edema develops in the gastrointestinal tract. However, because it takes a long time, 13.8 y...

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Dettagli Bibliografici
Pubblicato in:Clin J Gastroenterol
Autori principali: Honda, Daisuke, Ohsawa, Isao, Iwanami, Keiichi, Rinno, Hisaki, Tomino, Yasuhiko, Suzuki, Yusuke
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Singapore 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8298325/
https://ncbi.nlm.nih.gov/pubmed/33544288
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s12328-021-01338-1
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