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Increased Serum Interleukin-6 and Tumor Necrosis Factor Alpha Levels in Fabry Disease: Correlation with Disease Burden

OBJECTIVES: Fabry disease (FD) is an X-linked lysosomal disease caused by variants of the GLA gene; the formation of defective alpha-galactosidase A contributes to the accumulation of substrates in several organs. Chronic inflammation is thought to contribute to organ damage in FD patients. METHODS:...

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Detalhes bibliográficos
Publicado no:Clinics (Sao Paulo)
Main Authors: Rosa, Nilton Salles, Bento, Judith Campos de Barros, Caparbo, Valéria de Falco, Pereira, Rosa Maria Rodrigues
Formato: Artigo
Idioma:Inglês
Publicado em: Faculdade de Medicina / USP 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8266164/
https://ncbi.nlm.nih.gov/pubmed/34287477
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.6061/clinics/2021/e2643
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