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TAFRO Syndrome with Renal Thrombotic Microangiopathy: Insights into the Molecular Mechanism and Treatment Opportunities

TAFRO syndrome is an extremely rare form of idiopathic MCD, characterized by thrombocytopenia, anasarca, fever, reticulin fibrosis on bone marrow biopsy, and organomegaly. Like idiopathic MCD, renal involvement is also a common presentation in patients with TAFRO syndrome. Furthermore, membranoproli...

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Dades bibliogràfiques
Publicat a:Int J Mol Sci
Autors principals: Tu, Kun-Hua, Fan, Pei-Yi, Chen, Tai-Di, Chuang, Wen-Yu, Wu, Chao-Yi, Ku, Cheng-Lung, Tian, Ya-Chung, Yang, Chih-Wei, Fang, Ji-Tseng, Yang, Huang-Yu
Format: Artigo
Idioma:Inglês
Publicat: MDPI 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8230834/
https://ncbi.nlm.nih.gov/pubmed/34208103
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms22126286
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