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Pediatric hemophagocytic lymphohistiocytosis
Hemophagocytic lymphohistiocytosis (HLH) is a syndrome describing patients with severe systemic hyperinflammation. Characteristic features include unremitting fever, cytopenias, hepatosplenomegaly, and elevation of typical HLH biomarkers. Patients can develop hepatitis, coagulopathy, liver failure,...
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| Publicado en: | Blood |
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| Autores principales: | , |
| Formato: | Artigo |
| Lenguaje: | Inglês |
| Publicado: |
American Society of Hematology
2020
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| Materias: | |
| Acceso en línea: | https://ncbi.nlm.nih.gov/pmc/articles/PMC8212354/ https://ncbi.nlm.nih.gov/pubmed/32107531 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1182/blood.2019000936 |
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