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New familial cases of karyomegalic interstitial nephritis with mutations in the FAN1 gene

BACKGROUND: Karyomegalic interstitial nephritis (KIN) is a rare disease entity first described by Burry in 1974. The term KIN was introduced by Mihatsch et al. in 1979. KIN is characterized by chronic tubulointerstitial nephritis associated with enlarged tubular epithelial cell nuclei, which leads t...

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Bibliografski detalji
Izdano u:BMC Med Genomics
Glavni autori: Rejeb, Imen, Jerbi, Mouna, Jilani, Houweyda, Gaied, Hanène, Elaribi, Yasmina, Hizem, Syrine, Aoudia, Raja, Hedri, Hafedh, Zaied, Chiraz, Abid, Salwa, Bacha, Hassen, BenAbdallah, Taieb, BenJemaa, Lamia, Goucha, Rim
Format: Artigo
Jezik:Inglês
Izdano: BioMed Central 2021
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC8201669/
https://ncbi.nlm.nih.gov/pubmed/34126972
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12920-021-01009-7
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