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Gastrostomy for infants with severe epidermolysis bullosa simplex in neonatal intensive care

INTRODUCTION: Severe epidermolysis bullosa simplex (EBS sev) is a rare genodermatosis characterized by congenital generalized blistering and mucosal involvement. Increased needs and decreased intake quickly lead to nutritional imbalance. Enteral nutrition support is proposed, but classical nasogastr...

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Detalles Bibliográficos
Publicado en:Orphanet J Rare Dis
Main Authors: Marro, M., De Smet, S., Caldari, D., Lambe, C., Leclerc-Mercier, S., Chiaverini, C.
Formato: Artigo
Idioma:Inglês
Publicado: BioMed Central 2021
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC8196452/
https://ncbi.nlm.nih.gov/pubmed/34116697
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01896-0
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