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Design and rationale of a randomised, double-blind trial of the efficacy and safety of pirfenidone in patients with fibrotic hypersensitivity pneumonitis

Hypersensitivity pneumonitis (HP) is an immunologically mediated form of lung disease resulting from inhalational exposure to any of a large variety of antigens. A subgroup of patients with HP develops pulmonary fibrosis (fibrotic HP; FHP), a significant cause of morbidity and mortality. This study...

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Dades bibliogràfiques
Publicat a:ERJ Open Res
Autors principals: Fernández Pérez, Evans R., Crooks, James L., Swigris, Jeffrey J., Solomon, Joshua J., Mohning, Michael P., Huie, Tristan J., Koslow, Matthew, Lynch, David A., Groshong, Steve D., Fier, Kaitlin
Format: Artigo
Idioma:Inglês
Publicat: European Respiratory Society 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8181708/
https://ncbi.nlm.nih.gov/pubmed/34109243
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1183/23120541.00054-2021
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