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Case of an unreported genetic variant of salt losing 3-β-hydroxysteroid dehydrogenase deficiency

Salt losing 3-β-hydroxysteroid dehydrogenase deficiency (HSD3B2) is a rare form of congenital adrenal hyperplasia, seen in <0.5% of cases. We present a 7-year-old male diagnosed with HSD3B2 deficiency, not identified by state newborn screen, due to a novel variant identified in the HSD3B2 gene (c...

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Pubblicato in:Oxf Med Case Reports
Autori principali: Alkhatib, Einas H, Adams, Stacie D, Miller, Emily R
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8143666/
https://ncbi.nlm.nih.gov/pubmed/34055358
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/omcr/omab021
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