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Rare PHEX variant with insidious presentation leads to a delayed diagnosis of X-linked hypophosphatemia

A 7-year-old girl without a significant previous medical history was diagnosed with X-linked hypophosphatemic rickets (XLHR) due to a rare, most likely pathogenic, PHEX gene variant after a 4-year delayed diagnosis due to mild clinical presentation. At 2 years of age, her intoeing and femoral bowing...

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Pubblicato in:BMJ Case Rep
Autori principali: Constantacos, Cathrine, Hunter, Janel Darcy, Walsh, Elizabeth Tharpe, South, Andrew Michael
Natura: Artigo
Lingua:Inglês
Pubblicazione: BMJ Publishing Group 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8137255/
https://ncbi.nlm.nih.gov/pubmed/34011663
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bcr-2020-240336
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