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Lymphoproliferative malignancies in patients with neurofibromatosis 1

Neurofibromatosis 1 (NF1) is an inherited, autosomal-dominant, tumor predisposition syndrome with a birth incidence as high as 1:2000. A patient with NF1 is four to five times more likely to develop a malignancy as compared to the general population. The number of epidemiologic studies on lymphoprol...

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Detalhes bibliográficos
Publicado no:Orphanet J Rare Dis
Main Authors: Bergqvist, Christina, Hemery, François, Jannic, Arnaud, Ferkal, Salah, Wolkenstein, Pierre
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2021
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC8136208/
https://ncbi.nlm.nih.gov/pubmed/34011343
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s13023-021-01856-8
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