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The VEXAS Syndrome: Uncontrolled Inflammation and Macrocytic Anaemia in a 77-Year-Old Male Patient

The VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome is a recently described X-linked autoinflammatory condition caused by a somatic mutation of the UBA1 gene and characterized by an evolving phenotype. This includes inflammatory processes such as recurrent fever, Sweet’s sy...

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Pubblicato in:Eur J Case Rep Intern Med
Autori principali: Himmelmann, Andreas, Brücker, Rolf
Natura: Artigo
Lingua:Inglês
Pubblicazione: SMC Media Srl 2021
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC8112083/
https://ncbi.nlm.nih.gov/pubmed/33987129
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.12890/2021_002484
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