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Narrative review on Morbus Fabry: diagnosis and management of cardiac manifestations

Fabry disease (FD) is an X-linked lysosomal storage disorder due to reduced or undetectable α-galactosidase A (AGAL-A) enzyme activity caused by pathogenic variants in the AGAL-A gene (GLA). Tissue and organ changes are caused by widespread progressive accumulation of globotriaosylceramide (Gb(3)) a...

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Dades bibliogràfiques
Publicat a:Cardiovasc Diagn Ther
Autors principals: Linhart, Aleš, Paleček, Tomáš
Format: Artigo
Idioma:Inglês
Publicat: AME Publishing Company 2021
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC8102243/
https://ncbi.nlm.nih.gov/pubmed/33968642
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.21037/cdt-20-593
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