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Pregnancy in Familial Chylomicronemia Syndrome: Plasmapheresis as Therapeutic Approach
Introduction: Familial Chylomicronemia Syndrome (FCS) is a rare autosomal recessive disease where functional loss of lipoprotein lipase results in severe hypertriglyceridemia. Patients often experience recurrent acute pancreatitis, a life-threatening disease. Serum triglycerides (TGs) are physiologi...
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| Publicado no: | J Endocr Soc |
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| Main Authors: | , , , , , , , , , |
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Oxford University Press
2021
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC8090153/ https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jendso/bvab048.635 |
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