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Predicted Succinated Dehydrogenase Subunit Variant Pathogenicity: Why Are SDHB Variants “Bad”?

Variants in the 4 genes encoding subunits A-D of succinate dehydrogenase (SDH) are associated with paraganglioma and pheochromocytoma. Intuitively, loss-of-function variants affecting any of the subunits should equally diminish SDH function leading to succinate accumulation and tumorigenesis after l...

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Detalles Bibliográficos
Publicado en:J Endocr Soc
Main Authors: Gruber, Lucinda, Maher, L James
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2021
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC8089237/
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1210/jendso/bvab048.144
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